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Gene profile

LDLR

HGNC:6547 · SaudiVarKB evidence summary derived from retained literature mentions.

61Gene mentions
61Publications
36Linked variants
39Associated phenotypes

Associated phenotypes

Co-mentioned in LDLR publications

Linked variants

Variants normalized to LDLR
VariantHGVS / rsIDArticlesMentions
p.W577Cp.W577C33
c.1474G>Ac.1474G>A22
p.D492Np.D492N22
c.1429G>Ac.1429G>A22
p.D477Np.D477N22
c.2027delGc.2027delG22
p.C231*p.C231*11
p.R744*p.R744*11
c.335_336insCGAGc.335_336insCGAG11
p.F114Rfsp.F114Rfs11
c.622G>Ac.622G>A11
p.E208Kp.E208K11
p.Y419Dp.Y419D11
p.S202Tfsp.S202Tfs11
c.1731G>Tc.1731G>T11
c.1783C>Tc.1783C>T11
p.R595Wp.R595W11
c.9835A>Gc.9835A>G11
p.S3279Gp.S3279G11
p.G676Afsp.G676Afs11
1171G>A11
1167G>A11
c.2416dupc.2416dup11
p.Gln35Terp.Gln35Ter11
c.2416dupGc.2416dupG11
c.666_670dupc.666_670dup11
p.Ser3279Glyp.Ser3279Gly11
rs2228671rs222867111
rs72658855rs7265885511
rs5925rs592511
rs1529729rs152972911
rs688rs68811
c.1332dupc.1332dup11
p.D445*p.D445*11
c.1413A>Gc.1413A>G11
rs5930rs593011

Population context

Reported in the same publications

Supporting publications

61 records
  1. 2026Whole-exome sequencing in obstructive coronary artery disease identifies rare and novel variants in cardiac arrhythmia and pulmonary arterial hypertension-associated genes.Biomolecules & biomedicinePubMed ↗
  2. 2026Epiafzelechin, a Flavanol, Regulates Lipid Homeostasis Through Modulation of HMGCR, PCSK9, and PPAR-α: Mechanistic Insights and Therapeutic Implications.Cardiovascular therapeuticsPubMed ↗
  3. 2026Global survey of genetic testing methods for familial hypercholesterolemia. A study and recommendations from the EAS FHSC registry.European journal of preventive cardiologyPubMed ↗
  4. 2026Tumor-directed evolution of VSVΔ51M produces novel viruses with enhanced antitumor efficacy.Frontiers in molecular biosciencesPubMed ↗
  5. 2026Overcoming Barriers to Clinical Translation: MG1 Maraba Virus as an Emerging Platform for Oncolytic Immunotherapy.VirusesPubMed ↗
  6. 2026Apolipoprotein E in Alzheimer's disease: A review of APOE receptors, signalling pathways and therapeutic opportunities.Molecular and cellular neurosciencesPubMed ↗
  7. 2025Identification of variants in exon 4 of the LDLR gene and assessment of their effects on the produced proteins in saudi women with metabolic syndrome.Diabetology & metabolic syndromePubMed ↗
  8. 2025Homozygous familial hypercholesterolemia in a high-consanguinity population: Insights from a Saudi cohort.Journal of clinical lipidologyPubMed ↗
  9. 2025Gastric mucosal differentially expressed genes after bariatric surgery: Effects on sterol-related pathways.The Journal of steroid biochemistry and molecular biologyPubMed ↗
  10. 2025Multimodal Therapy Achieves Secondary Prevention LDL-C Targets in LDL-Receptor Null Homozygous Familial Hypercholesterolemia.JACC. Case reportsPubMed ↗
  11. 2025Charantin targets HMGCR-PCSK9 axis and activates PPAR-α signaling to ameliorate hyperlipidemia: Mechanistic insights from bioinformatics and in-vivo studies.PloS onePubMed ↗
  12. 2025Pathogenic LDLR Variants (c.103 C>T and c.2416dup) in ligand-binding and cytosolic domains in Saudi familial hypercholesterolemia: Molecular characterization and computational insights.Computational and structural biotechnology journalPubMed ↗
  13. 2025Whole exome sequencing identifies concurrent LDLR and ABCG8 mutations in a Saudi family with familial hypercholesterolemia and Sitosterolaemia.Frontiers in geneticsPubMed ↗
  14. 2025Structural dynamics of PCSK9 loss-of-function variants: implications for LDL cholesterol regulation and cardiovascular risk.Cellular and molecular biology (Noisy-le-Grand, France)PubMed ↗
  15. 2025Clinical exome sequencing identifies novel gene variants associated with ischemic stroke in the Saudi Tabuk population.Frontiers in human neurosciencePubMed ↗
  16. 2024The Effect of PCSK9 Inhibitors on LDL-C Target Achievement in Patients with Homozygous Familial Hypercholesterolemia: A Retrospective Cohort Analysis.Advances in therapyPubMed ↗
  17. 2024Berberine modulates cardiovascular diseases as a multitarget-mediated alkaloid with insights into its downstream signals using in silico prospective screening approaches.Saudi journal of biological sciencesPubMed ↗
  18. 2024Potential use of proprotein convertase subtilisin/kexin type 9 (PCSK9) inhibition and prevention method in viral infection.Microbial cell factoriesPubMed ↗
  19. 2024Viscosol Treatment Ameliorates Insulin-Mediated Regulation of Dyslipidemia, Hepatic Steatosis, and Lipid Metabolism by Targeting PTP1B in Type-2 Diabetic Mice Model.International journal of endocrinologyPubMed ↗
  20. 2023Identification and functional characterization of two rare LDLR stop gain variants (p.C231* and p.R744*) in Saudi familial hypercholesterolemia patients.Panminerva medicaPubMed ↗
  21. 2023Association of CELSR2, APOB100, ABCG5/8, LDLR, and APOE polymorphisms and their genetic risks with lipids among the Thai subjects.Saudi journal of biological sciencesPubMed ↗
  22. 2023Management and clinical outcomes of patients with homozygous familial hypercholesteremia in Saudi Arabia.Monaldi archives for chest disease = Archivio Monaldi per le malattie del toracePubMed ↗
  23. 2023Protein structural insights into a rare PCSK9 gain-of-function variant (R496W) causing familial hypercholesterolemia in a Saudi family: whole exome sequencing and computational analysis.Frontiers in physiologyPubMed ↗
  24. 2023Novel LDLR Variant in Familial Hypercholesterolemia: NGS-Based Identification, In Silico Characterization, and Pharmacogenetic Insights.Life (Basel, Switzerland)PubMed ↗
  25. 2022The rate of secondary genomic findings in the Saudi population.American journal of medical genetics. Part APubMed ↗
  26. 2022Identification of Novel and Known LDLR Variants Triggering Severe Familial Hypercholesterolemia in Saudi Families.Current vascular pharmacologyPubMed ↗
  27. 2022Edible Bird's Nest Regulates Hepatic Cholesterol Metabolism through Transcriptional Regulation of Cholesterol Related Genes.Evidence-based complementary and alternative medicine : eCAMPubMed ↗
  28. 2022PCSK9 pathway-noncoding RNAs crosstalk: Emerging opportunities for novel therapeutic approaches in inflammatory atherosclerosis.International immunopharmacologyPubMed ↗
  29. 2021Saudi Familial Hypercholesterolemia Patients With Rare LDLR Stop Gain Variant Showed Variable Clinical Phenotype and Resistance to Multiple Drug Regimen.Frontiers in medicinePubMed ↗
  30. 2021Bioinformatics analysis of rhinovirus capsid proteins VP1-4 sequences for cross-serotype vaccine development.Journal of infection and public healthPubMed ↗
  31. 2021Acaudina molpadioides mediates lipid uptake by suppressing PCSK9 transcription and increasing LDL receptor in human liver cells.Saudi journal of biological sciencesPubMed ↗
  32. 2020Heterozygosity in LDLR rs2228671 and rs72658855 Gene is Associated with Increased Risk of Developing Coronary Artery Disease in India -A Case-Control Study.Endocrine, metabolic & immune disorders drug targetsPubMed ↗
  33. 2020Zygophyllum album saponins prevent atherogenic effect induced by deltamethrin via attenuating arterial accumulation of native and oxidized LDL in rats.Ecotoxicology and environmental safetyPubMed ↗
  34. 2020Lomitapide for treatment of homozygous familial hypercholesterolemia: The Québec experience.AtherosclerosisPubMed ↗
  35. 2019Screening of common genetic variants in the APOB gene related to familial hypercholesterolemia in a Saudi population: A case-control study.MedicinePubMed ↗
  36. 2019Genetic testing for familial hypercholesterolemia: Impact on diagnosis, treatment and cardiovascular risk.European journal of preventive cardiologyPubMed ↗
  37. 2019LDLR Gene Polymorphisms (rs5925 and rs1529729) Are Associated with Susceptibility to Coronary Artery Disease in a South Indian Population.Medical sciences (Basel, Switzerland)PubMed ↗
  38. 2019Molecular Dynamics Simulation Reveals Exposed Residues in the Ligand-Binding Domain of the Low-Density Lipoprotein Receptor that Interacts with Vesicular Stomatitis Virus-G Envelope.VirusesPubMed ↗
  39. 2018In Silico Approach to Investigate the Structural and Functional Attributes of Familial Hypercholesterolemia Variants Reported in the Saudi Population.Journal of computational biology : a journal of computational molecular cell biologyPubMed ↗
  40. 2018LDLR rs688 TT Genotype and T Allele Are Associated with Increased Susceptibility to Coronary Artery Disease-A Case-Control Study.Journal of cardiovascular development and diseasePubMed ↗
  41. 2018Simplified Canadian Definition for Familial Hypercholesterolemia.The Canadian journal of cardiologyPubMed ↗
  42. 2018Utilizing Whole-Exome Sequencing to Characterize the Phenotypic Variability of Sickle Cell Disease.Genetic testing and molecular biomarkersPubMed ↗
  43. 2018Novel combined variants of LDLR and LDLRAP1 genes causing severe familial hypercholesterolemia.AtherosclerosisPubMed ↗
  44. 2017Compound heterozygous LDLR variant in severely affected familial hypercholesterolemia patient.Acta biochimica PolonicaPubMed ↗
  45. 2017Whole-Exomes Sequencing Delineates Gene Variants Profile in a Young Saudi Male with Familial Hypercholesterolemia: Case Report.Journal of clinical and diagnostic research : JCDRPubMed ↗
  46. 2017The Spectrum of Familial Hypercholesterolemia (FH) in Saudi Arabia: Prime Time for Patient FH Registry.The open cardiovascular medicine journalPubMed ↗
  47. 2017Interpreting the Mechanism of APOE (p.Leu167del) Mutation in the Incidence of Familial Hypercholesterolemia; An In-silico Approach.The open cardiovascular medicine journalPubMed ↗
  48. 2017The Genetic Spectrum of Familial Hypercholesterolemia (FH) in the Iranian Population.Scientific reportsPubMed ↗
  49. 2016Reducing Vascular Calcification by Anti-IL-1β Monoclonal Antibody in a Mouse Model of Familial Hypercholesterolemia.AngiologyPubMed ↗
  50. 2016Identification of a recurrent frameshift mutation at the LDLR exon 14 (c.2027delG, p.(G676Afs*33)) causing familial hypercholesterolemia in Saudi Arab homozygous children.GenomicsPubMed ↗
  51. 2016Human genome meeting 2016 : Houston, TX, USA. 28 February - 2 March 2016.Human genomicsPubMed ↗
  52. 2016Abstracts from the 3rd International Genomic Medicine Conference (3rd IGMC 2015) : Jeddah, Kingdom of Saudi Arabia. 30 November - 3 December 2015.BMC genomicsPubMed ↗
  53. 2015Vitamin B12 insufficiency induces cholesterol biosynthesis by limiting s-adenosylmethionine and modulating the methylation of SREBF1 and LDLR genes.Clinical epigeneticsPubMed ↗
  54. 2015Release of Vesicular Stomatitis Virus Spike Protein G-Pseudotyped Lentivirus from the Host Cell Is Impaired upon Low-Density Lipoprotein Receptor Overexpression.Journal of virologyPubMed ↗
  55. 2015Screening for genetic mutations in LDLR gene with familial hypercholesterolemia patients in the Saudi population.Acta biochimica PolonicaPubMed ↗
  56. 2014Identification of a novel nonsense variant c.1332dup, p.(D445*) in the LDLR gene that causes familial hypercholesterolemia.Human genome variationPubMed ↗
  57. 2013Correlation of SPECT imaging, biochemical parameters and mutation with systolic dysfunction.Genetics and molecular research : GMRPubMed ↗
  58. 2012The Arabic allele: a single base pair substitution activates a 10-base downstream cryptic splice acceptor site in exon 12 of LDLR and severely decreases LDLR expression in two unrelated Arab families with familial hypercholesterolemia.AtherosclerosisPubMed ↗
  59. 2010LDLR-Gene therapy for familial hypercholesterolaemia: problems, progress, and perspectives.International archives of medicinePubMed ↗
  60. 1997Distribution of HLA-DQ alpha and polymarker (LDLR, GC, GYPA, HBGG, and D7S8) alleles in Arab and Pakistani populations living in Abu Dhabi, United Arab Emirates.Journal of forensic sciencesPubMed ↗
  61. 1991Recurrent mutation at aa 792 in the LDL receptor gene in a French patient.Human geneticsPubMed ↗