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Gene profile

SGPL1

HGNC:10817 · SaudiVarKB evidence summary derived from retained literature mentions.

6Gene mentions
6Publications
2Linked variants
3Associated phenotypes

Associated phenotypes

Co-mentioned in SGPL1 publications
PhenotypeIdentifierArticlesMentions
nephrotic syndrome55
epilepsyHP:000125022
inborn error of metabolismHP:000193911

Linked variants

Variants normalized to SGPL1
VariantHGVS / rsIDArticlesMentions
c.665G>Ac.665G>A11
p.R222Qp.R222Q11

Population context

Reported in the same publications
Country / regionGroupCohortArticles
Saudi Arabia2
Not specified41
Not specified761
Saudi Arabia211

Supporting publications

6 records
  1. 2026Familial glucocorticoid deficiency due to a novel TXNRD2 variant: expanding the spectrum of a rare genetic cause.Frontiers in endocrinologyPubMed ↗
  2. 2024Factors influencing survival in sphingosine phosphate lyase insufficiency syndrome: a retrospective cross-sectional natural history study of 76 patients.Orphanet journal of rare diseasesPubMed ↗
  3. 2024Prevalence estimate of sphingosine phosphate lyase insufficiency syndrome in worldwide and select populations.Genetics in medicine openPubMed ↗
  4. 2020Responsiveness of sphingosine phosphate lyase insufficiency syndrome to vitamin B6 cofactor supplementation.Journal of inherited metabolic diseasePubMed ↗
  5. 2020MRI Spectrum of Brain Involvement in Sphingosine-1-Phosphate Lyase Insufficiency Syndrome.AJNR. American journal of neuroradiologyPubMed ↗
  6. 2019SGPL1 Deficiency: A Rare Cause of Primary Adrenal Insufficiency.The Journal of clinical endocrinology and metabolismPubMed ↗