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Gene profile

MAN2B1

HGNC:6826 · SaudiVarKB evidence summary derived from retained literature mentions.

3Gene mentions
3Publications
1Linked variants
4Associated phenotypes

Associated phenotypes

Co-mentioned in MAN2B1 publications
PhenotypeIdentifierArticlesMentions
intellectual disabilityHP:000124922
hearing lossHP:000036522
retinal dystrophyHP:000055611
lysosomal storage diseaseHP:000354111

Linked variants

Variants normalized to MAN2B1
VariantHGVS / rsIDArticlesMentions
c.2402dupGc.2402dupG11

Population context

Reported in the same publications
Country / regionGroupCohortArticles
Saudi Arabia1

Supporting publications

3 records
  1. 2026Early-Onset Retinal Dystrophy in Alpha-Mannosidosis: A Case Report.Case reports in ophthalmologyPubMed ↗
  2. 2024Exome sequence analysis identifies a homozygous, pathogenic, frameshift variant in the MAN2B1 gene underlying clinical variant of α-mannosidosis.Frontiers in geneticsPubMed ↗
  3. 2010Novel human pathological mutations. Gene symbol: MAN2B1. Disease: Mannosidosis, alpha.Human geneticsPubMed ↗