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Phenotype profile

Niemann-Pick disease

SaudiVarKB evidence summary derived from retained literature mentions.

19Phenotype mentions
19Publications
9Associated gene records
18Associated variant records

Associated gene records

Co-mentioned in the same publications
GeneIdentifier / contextArticlesMentions
NPC1HGNC:789766
SMPD1HGNC:1112033
ARHGNC:64411
PGDHGNC:889111
PCSK9HGNC:2000111
UCP1HGNC:1251711
NPC2HGNC:1453711
COG6HGNC:1862111
SOAT1HGNC:1117711

Associated variant records

Co-mentioned in the same publications
VariantIdentifier / contextArticlesMentions
H421YH421Y22
rs1800592rs180059211
rs10011540rs1001154011
rs3811791rs381179111
rs1805081rs180508111
rs1805082rs180508211
rs45539933rs4553993311
rs2270565rs227056511
W533RW533R11
L137PL137P11
L549PL549P11
K576NK576N11
S379PS379P11
R441XR441X11
R474WR474W11
F480LF480L11
A196PA196P11
W32XW32X11

Associated population records

Co-mentioned in the same publications
PopulationIdentifier / contextArticlesMentions
Saudi Arabia44
Saudi ArabiaCohort 49211
Population recordCohort 8511
Saudi ArabiaCohort 39411
Population recordCohort 2,02011
Saudi ArabiaCohort 12511

Supporting publications

19 records
  1. 2026Targeting Pathways Implicated in Cholesterol Metabolism for Novel Cancer Therapy.Cancers1 mentions
  2. 2026Nano-Based Therapeutics in Rare Disease Management: Current Perspectives, Challenges, and Unmet Needs.Current neuropharmacology1 mentions
  3. 2024Novel Mutation in Chromosome 11p15.4 Causing Niemann-Pick Disease Type A in a Saudi Child.Cureus1 mentions
  4. 2024CffDNA screening for Niemann-pick disease, type C1: a case series.Frontiers in medicine1 mentions
  5. 2023An overview of the role of Niemann-pick C1 (NPC1) in viral infections and inhibition of viral infections through NPC1 inhibitor.Cell communication and signaling : CCS1 mentions
  6. 2022Anti-TNF therapy for inflammatory bowel disease in patients with neurodegenerative Niemann-Pick disease Type C.Wellcome open research1 mentions
  7. 2022A Niemann-Pick Disease Type C2 with Severe Pulmonary Involvement and Limited Therapeutic Options: A Case Report.Children (Basel, Switzerland)1 mentions
  8. 2019Liposome-targeted recombinant human acid sphingomyelinase: Production, formulation, and in vitro evaluation.European journal of pharmaceutics and biopharmaceutics : official journal of Arbeitsgemeinschaft fur Pharmazeutische Verfahrenstechnik e.V1 mentions
  9. 2018Corrigendum to "Cause of death in patients with chronic visceral and chronic neurovisceral acid sphingomyelinase deficiency (Niemann-Pick disease type B and B variant): Literature review and report of new cases" [Mol. Genet. Metab. 118 (2016) 206-213].Molecular genetics and metabolism1 mentions
  10. 2018Secondary Hemophagocytic Syndrome Associated with COG6 Gene Defect: Report and Review.JIMD reports1 mentions
  11. 2018Association of Uncoupling Protein 1 (UCP1) gene polymorphism with obesity: a case-control study.BMC medical genetics1 mentions
  12. 2016Cause of death in patients with chronic visceral and chronic neurovisceral acid sphingomyelinase deficiency (Niemann-Pick disease type B and B variant): Literature review and report of new cases.Molecular genetics and metabolism1 mentions
  13. 2011Education and imaging. Hepatobiliary and pancreatic: Niemann-Pick disease.Journal of gastroenterology and hepatology1 mentions
  14. 2007Acid sphingomyelinase-deficient Niemann-Pick disease: novel findings in a Greek child.Journal of inherited metabolic disease1 mentions
  15. 2005Idiopathic nodular panniculitis in Niemann-Pick disease.Journal of the European Academy of Dermatology and Venereology : JEADV1 mentions
  16. 2004Preimplantation genetic diagnosis for Niemann-Pick disease type B.Prenatal diagnosis1 mentions
  17. 2002The demographics and distribution of type B Niemann-Pick disease: novel mutations lead to new genotype/phenotype correlations.American journal of human genetics1 mentions
  18. 2000Type A Niemann-Pick disease.Journal of the European Academy of Dermatology and Venereology : JEADV1 mentions
  19. 1990Prevalence of different types of lysosomal storage diseases in Saudi Arabia.Journal of inherited metabolic disease1 mentions